Congenital malformation of the pulmonary airways. Case reporte
Article Sidebar
Article Details
Authors
Publication Information
Keywords
cyst
respiratory distress
Abstract
Pulmonary malformations comprise various anomalies of the respiratory system, including congenital malformation of the pulmonary airway (CVMAP), formerly known as cystic adenomatous malformation, a rare abnormality in the development of the terminal airways. Diagnosis can be made from the prenatal period by gestational ultrasound, sometimes finding serious fetal repercussions such as hydrops fetalis. The clinical presentation is variable, from asymptomatic to severe pulmonary complications. It usually presents with respiratory distress in the newborn. We present the case of a female newborn with prenatal diagnosis. Physical examination, chest radiographs, and pulmonary tomography support the diagnosis. Histopathological study confirms the diagnosis.
Graph - Number of readers per month
Downloads
How to Cite
License
This work is licensed under a Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International License.
 |
This work is licensed under Creative Commons Attribution-NonCommercial-ShareAlike 4.0 International (CC BY-NC-SA 4.0) |
| Copyright notice |
 |
Authors will retain their copyright and assign to the journal the right of first publication of their work, which will be simultaneously subject to a Creative Commons Attribution-Noncommercial-ShareAlike 4.0 International license (CC BY-NC-SA 4.0) that allows third parties to share the work as long as its author and its first publication in this magazine are indicated. |
|
Authors may adopt other non-exclusive license agreements for the distribution of the version of the published work (eg: deposit it in an institutional repository or publish it in a monographic volume) provided that the initial publication in this journal is indicated. |
|
Authors are allowed and recommended to disseminate their work through the internet (eg, in institutional telematic files or on their website) before and during the submission process, which can lead to interesting exchanges and increase citations of the published work. (See The effect of open access). |
| About the Creative Commons license |
|
|
You are free to: |
|
Share — copy and redistribute the material in any medium or format. |
|
Adapt — remix, transform, and build upon the material. |
|
The licensor cannot revoke these freedoms as long as you follow the license terms. |
Under the following terms: |
 |
Attribution — You must give appropriate credit, provide a link to the license, and indicate if changes were made. You may do so in any reasonable manner, but not in any way that suggests the licensor endorses you or your use. |
 |
NonCommercial — You may not use the material for commercial purposes. |
 |
ShareAlike — If you remix, transform, or build upon the material, you must distribute your contributions under the same license as the original. |
| No additional restrictions — You may not apply legal terms or technological measures that legally restrict others from doing anything the license permits. |
References
Barazzone-Argiroffo C, Lascano Maillard J, Vidal I, Bochaton-Piallat ML, Blaskovic S, Donati Y, et al. New insights on congenital pulmonary airways malformations revealed by proteomic analyses. Orphanet Journal of Rare Diseases. 2019 Nov 28;14(1)
Medina Valdivia JL. Congenital malformation of the pulmonary airway (MCVAP), Case Report. Revista de la Facultad de Medicina Humana. 2021 Jan 12;21(1):202–6.
Wong KKY, Flake AW, Tibboel D, Rottier RJ, Tam PKH. Congenital pulmonary airway malformation: advances and controversies. The Lancet Child & Adolescent Health. 2018 Apr;2(4):290–7.
Oermann CM, MD. Congenital pulmonary airway malformation. UpToDate [Internet]. www.uptodate.com. [cited 2022 Jul 17]. Available from: https://www.uptodate.com/contents/congenital-pulmonary-airway-malformation/print?search=malformacion